Introduction
70-kd Zeta-associated protein.
PMID: 16938520
an important negative prognostic factor in
chronic lymphocytic leukemia (CLL).
PMID: 17038529
one of the most studied prognostic markers in
Chronic Lymphocytic Leukemia (CLL).
PMID: 16906579
plays a pivotal role in interferon-stimulated
MAPK activation.
PMID: 16219325
a surrogate marker for immunoglobulin
heavy-chain variable region (IgV(H)) mutation status, which is
known as a prognostic marker in B-cell chronic lymphocytic
leukemia (CLL).
PMID: 16906585,
PMID: 16906582
a member of the Syk/ZAP protein tyrosine
kinase family, normally expressed in T cells and NK cells but
not found in normal, mature B cells.
PMID: 15871558,
PMID: 9535797
Normal Expression
Among normal B-cell subsets, ZAP-70 was found
expressed in normal pro/pre B cells but not in a significant
proportion of normal B cells with mature phenotype.
PMID: 16467082
ZAP-70 gene is normally expressed in T and
natural killer cells, where it is required for the T-cell
receptor (TCR) signaling.
PMID: 16467082
ZAP-70 is expressed in a subpopulation of
tonsillar and splenic normal B-lymphocytes that express an
activated phenotype. Furthermore, ZAP-70 expression can be
induced in vitro upon stimulation of blood and tonsillar B
cells.
PMID: 15800671
ZAP-70 is a tyrosine kinase expressed in
normal T cells and NK cells.
PMID: 15487457
By immunoblot and immunoprecipitation assay
using various anti-ZAP-70 antibodies, a 66 kDa tyrosine kinase
was detected in lysates from rat brain. During the development
of rat brain, expression levels of this 66 kDa tyrosine kinase
were highest around 3 weeks after birth and decreased thereafter
in the adult. In addition, immunoblot analysis demonstrated that
this 66 kDa tyrosine kinase was expressed almost solely in the
nervous system.
PMID: 9535797
Initial experiments in epithelial cells
indicated that ZAP-70 is diffusely located throughout the
quiescent cell, and accumulates at the plasma membrane upon
cellular activation. Intriguingly, a large amount of ZAP-70,
both chimeric and endogenous, resides in the nucleus of
quiescent and activated cells. Nuclear ZAP-70 becomes tyrosine
phosphorylated upon stimulation via the T cell receptor,
indicating that it may have an important biologic function.
PMID: 9362531
Abnormal Expression
ZAP-70 is expressed by many lymphoma types,
correlates with immunoglobulin heavy-chain variable region gene
mutational status in chronic lymphocytic leukemia/small
lymphocytic lymphoma (CLL/SLL), and can be detected reliably
using immunohistochemical methods.
PMID: 15133473
Function
high levels of ZAP-70 correlated with Binet
stages B or C indicating an involvement of ZAP-70 in mechanisms
promoting growth of B-CLL cells.
PMID: 15370248
ZAP-70 plays an important role in growth,
differentiation, and function of not only T cells but also nerve
cells and several embryonic tissues.
PMID: 7553892
Diagnostic and Therapeutic Value
immunohistological detection of ZAP-70 on
formalin-fixed BM biopsies at diagnosis appears a useful
methodological approach to identify patients with poor prognosis
in chronic lymphocytic leukaemia (CLL).
PMID: 17082778
ZAP-70 reactivity using a T-cell marker as a
control allows to identify the majority of patients with an
unmutated Ig VH genotype.
PMID: 17051526
although ZAP-70 positivity correlates with
IgV(H) mutation status and survival, variations in sample
handling and preparation may influence results. ZAP-70 testing
should not be used as the sole criterion for stratifying
patients for therapy.
PMID: 16906585
Patients with a low percentage (<20%) of
ZAP-70 positive neoplastic B lymphocytes have a much better
prognosis that those with a higher proportion (>20%) of ZAP-70
positive neoplastic B lymphocytes.
PMID: 16906580
ZAP-70 expression could become a key
parameter to guide patients towards risk adapted treatment
strategies in prospective clinical trials.
PMID: 16906579
ZAP-70 protein determined by flow cytometry
improves the prognostic significance of cytogenetics and appears
to be a better predictor of outcomes than IgV(H) gene mutational
status.
PMID: 16601244
ZAP-70 expression is not a CLL-specific
feature among B-cell malignancies and suggest that the absence
of ZAP-70 rather than its presence should be considered abnormal
for malignant B lymphocytes.
PMID: 16482211
ZAP-70 immunoreactivity can be a reliable
prognostic marker in chronic lymphocytic leukemia (CLL) and
proposes a system for evaluating the results. The observations
support the inclusion of the immunohistochemical expression of
ZAP-70 in clinical trials involving CLL patients.
PMID: 16321853
ZAP-70 protein, which can be measured by flow
cytometry in the general laboratory, is a reliable prognostic
marker in chronic lymphocytic leukaemia (CLL), equivalent to
that of IgVH gene mutational status.
PMID: 14726163
Review Articles
Functional and prognostic role of ZAP-70 in
chronic lymphocytic leukaemia.
PMID: 16300468
ZAP-70 in B cell malignancies.
PMID: 16263570
Applications
Flow Cytomery (FC)
Fifty-three consecutive B-CLL cases were
included in the study. ZAP-70 expression was investigated by
flow cytometry.
PMID: 17051526
National standardization of ZAP-70
determination by flow cytometry: The French experience.
PMID: 17041946
Evaluation of ZAP-70 expression by flow
cytometry in chronic lymphocytic leukemia: A multicentric
international harmonization process.
PMID: 16906588
Flow cytometric analyses for ZAP-70 were
performed in peripheral blood samples from 145 B-CLL (124 with
IgV(H) mutations) by a standard three-color protocol.
PMID: 16906587
We developed a system using the 8-peak
Rainbow beads as our fluorescence calibrator along with a fixed
cell control. Using a panel of CD19-PE, CD5-FITC, and
ZAP-70-Alexa 647, we stained normal whole blood, and blood and
bone marrow from patients with CLL to determine the level of
ZAP-70 expression in T-cell, B-cell, and CLL-cell populations.
PMID: 16906586
Use of a blocking antibody method for the
flow cytometric measurement of ZAP-70 in B-CLL.
PMID: 16906584
flow cytometric analysis of ZAP-70 suffers
from difficulties in standardization and interpretation. We
applied the Kolmogorov-Smirnov (KS) statistical test to make
analysis more straightforward.
PMID: 16906582
An optimized whole blood method for flow
cytometric measurement of ZAP-70 protein expression in chronic
lymphocytic leukemia.
PMID: 16906581
Comparison of bone marrow and peripheral
blood ZAP-70 status examined by flow cytometric
immunophenotyping in patients with chronic lymphocytic leukemia.
PMID: 16906578
We compared different staining methods
utilizing monoclonal antibodies (moAb) against ZAP-70:
anti-ZAP-70 PE, clone 1E7.2, anti-ZAP-70 PE, clone 17A/P-ZAP70
directly stained with flourochrome as well as anti-ZAP-70
antibody, clone 2F3.2 stained with Zenontrade mark Alexa
Fluor(R) 488 Labeling Kit.
PMID: 16906577
different gating strategies for determining
flow cytometric ZAP-70 expression status produce highly
discordant results. Further standardization is required before
ZAP-70 can be used as a reliable prognostic parameter in
immunophenotyping of B-CLL.
PMID: 16906574
ZAP-70 by flow cytometry: a comparison of
different antibodies, anticoagulants, and methods of analysis.
PMID: 16906573
Feasibility of an easily applicable method of
ZAP-70 measurement in chronic lymphocytic leukemia in the
routine flow cytometry setting: a methodological approach.
PMID: 16871389
Quantitative flow cytometry of ZAP-70 levels
in chronic lymphocytic leukemia using molecules of equivalent
soluble fluorochrome.
PMID: 16456869
A robust ratio metric method for analysis of
Zap-70 expression in chronic lymphocytic leukemia (CLL).
PMID: 16342060
Comparison of flow cytometric methods for the
measurement of ZAP-70 expression in a routine diagnostic
laboratory.
PMID: 16048494
Immunocytochemistry (ICC)
We modified the method of immunocytochemical
assessment of ZAP-70 expression. The traditional two-step method
with monoclonal anti-ZAP-70 antibody in the first step followed
by FITC-conjugated goat anti-mouse IgG was changed for one-step
method with monoclonal anti-ZAP-70 antibody labeled by Zenon
Alexa Fluor 488.
PMID: 15871558
Immunohistochemistry (IHC)
ZAP-70 expression, as detected by
immunohistochemistry on bone marrow biopsies from early-phase
chronic lymphocytic leukemia (CLL) patients, is a strong adverse
prognostic factor.
PMID: 17082778
The expression of ZAP-70, detected by an
immunohistochemical assay and also by real-time quantitative
reverse transcriptase-polymerase chain reaction assigned 83% of
the chronic lymphocytic leukemia cases to the suspected
immunoglobulin mutation subtype.
PMID: 16938520
The aim was to determine the prognostic
significance of the immunohistochemical expression of ZAP-70
protein in chronic lymphocytic leukemia (CLL) by means of the
long-term follow-up of 108 patients.
PMID: 16321853
Immunohistochemical analysis represents an
effective method for assessing ZAP-70 expression and reveals
that a variety of B-cell malignant neoplasms express ZAP-70,
albeit at low frequency.
PMID: 16280661
In this study ZAP-70 expression was studied
by immunohistochemistry in a spectrum of B-cell lymphoid
neoplasms; this staining method was compared with flow cytometry,
and the relationship of ZAP-70 expression to mutational status
and prognosis was assessed.
PMID: 15685592
We examined 446 specimens representing a
range of hematopoietic malignant neoplasms for ZAP-70 expression
by immunohistochemical analysis.
PMID: 15487457
Using immunohistochemical methods, we
evaluated zeta-associated protein (ZAP)-70 expression in 341
cases of non-Hodgkin and Hodgkin lymphoma.
PMID: 15133473
Immunoprecipitation (IP)
By immunoblot and immunoprecipitation assay
using various anti-ZAP-70 antibodies, a 66 kDa tyrosine kinase
was detected in lysates from rat brain.
PMID: 9535797
Western Blotting (WB)
ZAP-70 expression was ascertained by flow
cytometry, immunofluorescence, Western blot, and quantitative
reverse transcription-PCR.
PMID: 16467082
The expression of ZAP-70 was analyzed in
T-cell and B-cell lines and in peripheral-blood samples from 56
patients with CLL with the use of flow cytometry, Western
blotting, and immunohistochemistry.
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