The alveoli are lined with two types of cell, the Type I and Type II pneumocytes.
The Type I pneumocyte is a very large, thin cell stretched over a very large area. This cell cannot replicate and is susceptible to a large number of toxic insults. Type I pneumocytes are responsible for gas exchange occurring in the alveoli.
The Type II granular pneumocyte is a roughly cuboidal cell that is usually found at the alveolar septal junctions. Type II cells cover about 5% of the surface area of the alveoli, whereas type I pneumocytes (because of their squamous shape) cover 95% of the total area. Even though they cover less surface area, type II cells greatly outnumber type I cells. Type II cells are responsible for the production and secretion of surfactant. The Type II pneumocyte can replicate in the alveoli and will replicate to replace damaged Type I pneumocytes.
Alkaline
Phosphatase
Heat-stable alkaline phosphatase is a marker for human and
monkey type-I pneumocytes.
PMID: 2357723
a typical marker of type II pneumocyte
maturation.
PMID: 8761368
Aquaporin 5 (Aqp-5)
a
type-I pneumocyte
marker.
PMID: 15917467,
PMID: 11748153
present on the apical membrane of epithelial
cells in various secretory glands as well as on the apical
membrane of the airway epithelium, airway submucosal glands, and
type 1 pneumocytes, where it can participate in respiratory
tract water homeostasis.
PMID: 15536076
localized to the apical plasma membrane of
type I pneumocytes and the apical plasma membranes of secretory
epithelium in upper airway and salivary glands.
PMID: 9374640
Bauhinia purpurea lectin (BPL)
a
type I pneumocyte-specific
marker.
PMID: 7894248,
PMID: 8088898
Caveolins (Cav-1, -2, and -3)
a gene family of cytoplasmic
membrane-anchored scaffolding proteins that: (i) help to sculpt
caveolae membranes from the plasma membrane proper; and (ii)
participate in the sequestration of inactive signaling
molecules.
PMID: 9662443
caveolin-1 (also called caveolin, Cav-1 and
VIP2I) are found in terminally-differentiated cell types, such
as adipocytes, endothelia, smooth muscle cells, and type I
pneumocytes.
PMID: 15003112
Caveolin-2 (Cav-2) is colocalized and
coexpressed with Cav-1 and requires Cav-1 for proper membrane
targeting.
PMID: 15003112
In the adult, caveolin-1 and -2 are
co-expressed and are most abundant in type I pneumocytes,
endothelia, fibroblastic cells and adipocytes, while the
expression of caveolin-3 is restricted to striated muscle cells.
PMID: 9662443
CD44v6
marker for type II pneumocytes.
PMID: 15974816
Strong positivity for
CD44v6 was observed in the basal cells of bronchial epithelium,
squamous metaplasia, and type II pneumocytes.
PMID: 12940087,
PMID: 9224749
Nonneoplastic adult
lung showed CD44v6 expression that was restricted to epithelial
cells with membranous staining of basal bronchial cells and
squamous metaplasia as well as basolateral membranous staining
of type 2 pneumocytes.
PMID: 9210706
CD44v isoforms
containing exon v6 and v9 encoded epitopes are selectively
detectable in normal epithelial cells with a strong basolateral
distribution pattern in the entire population of type II
pneumocytes and in basal cells of the bronchial epithelium, and
it may be utilized by type II pneumocytes in epithelial-mesenchymal
interactions and in the maintenance of the pulmonary
histoarchitecture.
PMID: 7576702
CD208 (DC-LAMP)
may serve as a marker for pneumocyte
maturation in the developing fetal lung.
PMID: 16899762,
PMID: 16510184
a member of the
lysosomal associated membrane protein (LAMP) family,
is a
marker of normal and transformed type II pneumocytes.
PMID: 14982840
CP4
a
pneumocyte-derived collagenous surfactant-associated protein.
PMID: 3219363
Cx43
detected in pneumocytes type II and I, in
large blood vessel endothelia, in peribronchial smooth muscle
cells, and in some peribronchial and perivascular interstitial
cells. In severely injured lungs (about 3 months after
irradiation), Cx43 was found also in the cytoplasm of type II
pneumocytes.
PMID: 8911970
DC-LAMP (CD208)
constitutively
expressed by mouse, sheep, and human type II pneumocytes,
is a
marker of normal and transformed type II pneumocytes.
PMID: 14982840
gp600
the reactive epitopes for anti-gp600 in lung
parenchyma are exclusively localized on type II pneumocytes and
have a Mr of approximately 270 to 290 kDa and that anti-gp600
may be used as a specific immunologic marker for the type II
pneumocytes.
PMID: 2647848
HTI56
a marker of terminally
differentiated type I pneumocytes.
PMID: 10706135
ICAM-1
ICAM-1 detectable in the normal lung, was
also detected on the pneumocyte cell surface at all stages of
acute rejection, suggesting that pneumocytes were target cells
for LFA-1 positive cells.
PMID: 7959589
Neopterin-induced expression of intercellular adhesion
molecule-1 (ICAM-1) in type II-like alveolar epithelial cells.
PMID: 10594564
KL-6
a mucin-like
glycoprotein expressed on type II pneumocytes.
PMID: 14738246
one of the MUC1
antigens, is a mucin-like high-molecular-weight glycoprotein,
which is strongly expressed on type II pneumocytes.
PMID: 12924525
a mucin-like high molecular weight
glycoprotein secreted by proliferating type II alveolar
pneumocytes, has been identified as a potential marker of
interstitial pneumonitis.
PMID: 11927785
a mucin-like high-molecular-weight
glycoprotein, is expressed on type-2 pneumocytes and bronchiolar
epithelial cells.
PMID: 11557124,
PMID: 10733471
a mucin-like glycoprotein that is strongly
expressed on type II pneumocytes in the lung.
PMID: 10782818,
a MUC1 mucin preferentially expressed in
regenerating type 2 pneumocytes.
PMID: 9415357
MUC1
marker for type II pneumocytes.
PMID: 15974816
a powerful new marker for the type II
pneumocyte cell lineage that allows us to follow the type II
pneumocyte lineage during the process of lung carcinogenesis.
PMID: 9850098
marker of the type II pneumocyte progenitor
cell lineage.
PMID: 11948134,
PMID: 10706135
RAGE (receptor
for advanced glycation end products)
In normal lung low expression of the receptor
was observed in bronchiolar epithelia, type II pneumocytes,
macrophages and some endothelia. In all pathological conditions
associated with inflammation and lung damage overexpression of
both the receptor and of AGEs was observed in bronchiolar
epithelia, type II alveolar pneumocytes, alveolar macrophages
and endothelia.
PMID: 16941014
a cell surface multiligand receptor of the
immunoglobulin superfamily, expressed in the cytoplasm of
pneumocytes.
PMID: 15933755
Anti-RAGE immunoreactivity was prominent in
alveolar epithelial type I pneumocytes, while it was absent from
type II pneumocytes and capillary endothelium.
PMID: 9846897
Surfactant Protein A,
B, C, and D
surfactant protein A (SP-A) is a distinct
marker for type II pneumocytes.
PMID: 12924525
SP-A production is a marker of type II
pneumocyte differentiation.
PMID: 10745024
SP-A is a major
pulmonary surfactant protein produced by type II pneumocytes.
PMID: 8425584
Surfactant protein
(SP)-B expression is restricted to type II pneumocytes and Clara
cells in the lung.
PMID: 11152647
surfactant protein C is a type II pneumocyte-specific
gene.
PMID: 15268776,
PMID: 9498406
surfactant protein-D (SP-D) is produced by
type II pneumocytes.
PMID: 11061091
T1alpha
a
type I pneumocyte
marker.
PMID: 11748153
Thomsen-Friedenreich antigen
marker for type II
pneumocytes.
PMID: 15974816,
PMID: 10603446
TF antigen
directly expressed on
the apical surface of some type II pneumocytes in the pulmonary
sarcoidosis specimens.
PMID: 10453879
express abundantly in
type II pneumocytes.
PMID: 10071237
In patients with IPF,
IP-SSc, and idiopathic BOOP, the TF antigen was positively
stained in type II pneumocytes and in some alveolar macrophages.
Neither TF antigens nor TF-mRNA were detected in the normal
lung. These results indicate that type II pneumocytes are a
major source of TF, suggesting that TF production in these cells
is closely related to fibrin deposition in the lungs of people
with these diseases.
PMID: 9279250
Thyroid Transcription Factor 1 (TTF-1)
marker for type II pneumocytes.
PMID: 15974816
a 38-kd homeodomain
containing DNA-binding protein originally identified in
follicular cells of the thyroid and subsequently in pneumocytes.
PMID: 12051643
a 38-kd protein,
located primarily in the nucleus of type 2 pneumocytes and clara
cells.
PMID: 11679943,
PMID: 11075855